[Successful Staged Total Aortic Replacement in a Young Patient with Marfan Syndrome:Report of a Case].
We report a case of a young male patient diagnosed with Marfan syndrome who presented with lower limb ischemia due to Stanford type B aortic dissection. Initial imaging revealed significant dilation of the aortic root and occlusion of the right iliac artery. Surgical treatment was performed in three stages:revascularization of the lower limbs, valve-sparing aortic root and total arch replacement, and finally thoracoabdominal aortic replacement. This stepwise approach prioritized organ perfusion and allowed for safe and effective repair of the extensive aortic pathology. The postoperative course was uneventful, and the patient remains in good condition. This case highlights the importance of staged surgical strategy in complex aortic disease associated with Marfan syndrome.